Combined replacement effects of human modified β-hexosaminidase B and GM2 activator protein on GM2 gangliosidoses fibroblasts
K Kitakaze, C Tasaki, Y Tajima, T Hirokawa… - … and Biophysics Reports, 2016 - Elsevier
... were dissociated and sonicated with phosphate-buffered saline [PBS; 8.1 mM Na 2 HPO 4
(Sigma-Aldrich), 1.5 mM KH 2 PO 4 (Wako), 137 mM NaCl, 2.7 mM KCl, pH 7.4] containing 1%
(v/v) Nonidet P-40 and protease inhibitors [1 µM pepstatin A (Peptide Institute, Osaka, Japan ...
(Sigma-Aldrich), 1.5 mM KH 2 PO 4 (Wako), 137 mM NaCl, 2.7 mM KCl, pH 7.4] containing 1%
(v/v) Nonidet P-40 and protease inhibitors [1 µM pepstatin A (Peptide Institute, Osaka, Japan ...
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